WHAT IS THE KT SYNDROME?
The KT (Klippel-Trenaunay) syndrome is a congenital mesodermal abnormality consisting of a capillary nevus (port wine stain) that can be extensive; venous anomalies (lack of venous valves in the deep vein even total lack (agenesis ) or partial lack (hypoplesia) of deep veins, congenital varicose veins that can represent the only venous drainage of the limb, swelling and limb hypertrophy. The treatment is only symptomatic. Removal of the external varicosities should be done only after the deep veins have been fully studied and visualized. If they represent the only outflow tract, removal could have catastrophic consequences. The Parkes-Weber syndrome is similar but here one can find clinical and radiographic evidence of clear A-V malformations /fistulas. For additional info you have to do a literature search. Read: Ann Surg 1988; 207:213-218 and Br J Surg 1985;72:232-36.
