What is the severity of Haemophilia?
The severity of the disorder varies, and it is related to the amount of clotting factor present in the blood. Usually the deficiency level of the factor is the same or similar in the sons of a carrier woman. The normal range of Factor VIII or IX is 50 per cent to 150 per cent in those unaffected. In those affected there are three basic deficiency levels: Severe, moderate and mild. How is diagnosis made? First, a detailed personal and family history is made, relating to questions regarding unusual bruising or prolonged bleeding after tooth extractions or tonsillectomy. Prolonged bleeding should arouse suspicions of Haemophilia or other blood related problems. Second, screening tests for Hemostatis like bleeding time, activated partial thromboplastin time (APTT), prothrombin ratio, etc. should be done. What does one do in the management of bleeds? Ideally, “when in doubt, treat” is the rule. Bleeds in the joints, soft tissues, nose, mouth and gums are minor bleeds. Bleeds in the central
