What is hereditary paraganglioma-pheochromocytoma syndrome?
Hereditary paraganglioma-pheochromocytoma syndrome (PGL/PCC) is a group of familial cancer syndromes characterized by the presence of: • Paragangliomas (PGL) — tumors that arise from neuroendocrine tissues symmetrically distributed along the spine from the base of the skull to the pelvis • Pheochromocytomas (PCC) — a type of paraganglioma that is confined to the adrenal gland, a small hormone producing organ located on top of each kidney Continue reading to learn about the subtypes of paragangliomas, typical symptoms, causes of paraganglioma-pheochromocytoma syndrome, and how the syndromes are inherited.
