What is an anomalous coronary artery (ACA)?
An anomalous coronary artery (ACA) is a coronary artery that has an abnormality or malformation. The malformation is congenital (present at birth) and is most often related to the origin or location of the coronary artery. However, there may be other defective areas in the coronary artery. Likewise, it may affect the overall size and shape of the affected coronary artery or arteries. ACA may also occur along with other congenital heart defects. This condition may also be called congenital coronary artery anomaly (CAA). Although they are present at birth, ACAs are often not diagnosed until late adolescence or adulthood, because of the lack of symptoms or because symptoms may not be recognized as being caused by ACA. Teens or adults with unknown ACA may have an initial episode of chest pain, heart failure, or even sudden cardiac death before the condition is recognized. Anomalous coronary arteries occur in approximately 5 percent of people undergoing cardiac catheterization to evaluate c