What is a bronchopulmonary sequestration (BPS or pulmonary sequestration)?
A BPS is a benign mass of non-functioning lung tissue that appears during early lung development. This lesion has no connection with the airway and receives its blood supply from the systemic circulation usually off the abdominal or thoracic aorta. The most common type of BPS is formed within the normal lung itself and is referred to as intralobar. The other type of BPS is known as extralobar, and is formed outside the normal lung. This type of lesion is usually found in the chest cavity although rarely it may be found in the abdomen. There is a higher incidence of associated anomalies in babies with extralobar BPS. Other anomalies often present with extralobar BPH include a congenital diaphragmatic hernia (CDH), pectus excavactum, tracheoesophageal fistula, esophageal duplication and congenital heart disease. What testing is recommended during the pregnancy? Serial ultrasounds will monitor the size of the baby’s BPS and rule out other anomalies. Color flow Doppler ultrasound evaluatio
