Should blood vessel tumors occurring in CNS sites be coded to blood vessel or CNS?
They should be coded to the CNS site in which they occur. This follows the same rationale that if you have a lymphoma of the brain, it is coded to “brain,” not lymph node. Example: Patient is diagnosed with a hemangioblastoma of the right temporal lobe of the brain. Site code: C71.2, histology code: 9161/1 Laterality: Right only. Angiosarcomas are exceedingly rare and occur in the “brain” parenchyma. Hemangiopericytomas are not rare tumors and occur almost entirely attached to the dura (meninges). There have been rare case reports of hemangioendotheliomas of the brain. They occur anywhere in the brain and dura.
