How are Naegeli syndrome and dermatopathia pigmentosa reticularis similar?
Naegeli Syndrome- A rare autosomal dominant form of ectodermal dysplasia Dermatopathia Pigmentosa Reticularis- A rare autosomal dominant congenital disorder that is a form of ectodermal dysplasia. Well, they both are a rare autosomal dominant form of ectodermal dysplasia, thats one similarity. Another similarity is that they are both caused by a specific deficiency in the keratin 14 protein.