Does Dejerine-Sottas affect the brain?
Short answer: No. Dejerine-Sottas is a disease of the peripheral nervous system, not the central nervous system. Intelligence is normal. Slightly longer answer: Of course, that does not preclude the existence of other conditions affecting intelligence. Long answer: I can find one article describing a case where Dejerine-Sottas was linked to schizophrenic symptoms (A case of Dejerine-Sottas disease with schizophrenic symptoms: A clinical and pathological study, also see the original Japanese version). Another article presents A case of Dejerine-Sottas disease with prominent ataxia and brain stem involvement. A clinical, electrophysiological, otoneurologic, and ultrastructural study. but notes that higher structures were not affected. Lastly, this article (also in Japanese) describes A case of Dejerine-Sottas disease with central nervous system involvement, but since there is no translation available, I have no further details at this time. In any case, involvement of the brain in Dejeri
