Do you know what the cause of sensorineural hearing loss in OI is?
No one is sure why OI carries a greater risk of hearing loss. It may be that the bone turnover around the cochlea (the inner ear) releases enzymes into the inner ear that damage it. This is just speculation though. Q: Do you usually see different types of hearing loss and ages for hearing loss within a family of OI Type I? A: You can see both conductive and sensorineural hearing loss with all types of OI. They can vary in a family just as much as between unrelated people. Q: Is there a difference between the ages of onset for either type of hearing loss? A: Sensorineural hearing loss tends to be more frequent as one ages. The conductive loss usually occurs in the 20s and 30s, but these are generalizations that have many exceptions. Q: Our 24-year-old son, whose hearing is rapidly deteriorating, has an appointment with an audiologist. Are there any special tests that he should ask for because he has OI? A: The only tests are routine hearing tests with air and bone conduction and the spe
