How Common/Rare is ET?
The published annual incidence for ET ranges from 0.1-2.4/100,000. It is rare and is classified as an orphan disease. Mesa RA, Tefferi A et al, The incidence and epidemology of essential thrombocythemia and agnogenic myeloid metaplasia: an Olmstead Country study. Blood 1997; 90 (supp 1): abstract 1547; Chaiter Y et al, High incidences of myeloproliferative disorders is Ashkezi Jews in Northern Israel, Leuk Lymph 1992; 7:251-255; Dougan LE et al, The effect of diagnostic review on the estimated incidence of lymphatic and hematopoitic neoplasms in Western Australia. Cancer 1981; 48:866-872.
